Internal Medicine
Online ISSN : 1349-7235
Print ISSN : 0918-2918
ISSN-L : 0918-2918
CASE REPORTS
Peripheral T Cell Lymphoma with a High Titer of Proteinase-3-Antineutrophil Cytoplasmic Antibodies that Resembled Wegener's Granulomatosis
Tsuyoshi ShiraiReiko TakahashiYumi TajimaKatsura KohataJoji YamamotoHiroshi FujiiNaruhiko TakasawaKenichi IshizawaRyo IchinohasamaTomonori IshiiHideo Harigae
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JOURNAL OPEN ACCESS

2009 Volume 48 Issue 23 Pages 2041-2045

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Abstract

Here, we present a 54-year-old man with proptosis and swelling below the left eyelid. Laboratory findings showed high levels of PR3-ANCA and histological examination of the first biopsy revealed acute inflammation. Together with the findings of MRI, a diagnosis of WG was made. However, the disease progressed rapidly and histological examination of the second biopsy revealed infiltration of neoplastic T lymphocytes with aberrant loss of CD7. A final diagnosis of peripheral T cell lymphoma, not otherwise specified (WHO) was made, and complete remission was achieved by chemotherapy. This is a very rare case of T cell lymphoma with a high titer of PR3-ANCA.

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© 2009 by The Japanese Society of Internal Medicine
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