JAPANESE CIRCULATION JOURNAL
Online ISSN : 1347-4839
Print ISSN : 0047-1828
ISSN-L : 0047-1828
Case Report
Surgical Treatment for Scheie's Syndrome (Mucopolysaccharidosis Type I-S)
Report of Two Cases
Kenji MinakataYutaka KonishiMasahiko MatsumotoSenri Miwa
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1998 Volume 62 Issue 9 Pages 700-703

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Abstract

Scheie's syndrome (mucopolysaccharidosis type I-S) is a rare genetic lysosomal storage disease affecting mucopolysaccharide metabolism, and is known to include cardiovascular disease. Surgical treatment was carried out in 2 patients with Scheie's syndrome. Patient 1 was a 56-year-old man with triple-vessel coronary artery disease, who successfully underwent coronary artery bypass grafting. Patient 2 was a 52-year-old man with aortic and mitral valve stenosis, who successfully underwent combined aortic and mitral valve replacement. The literature on Scheie's syndrome associated with valvular and coronary artery disease is also reviewed. (Jpn Circ J 1998; 62: 700 - 703)

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© 1998 THE JAPANESE CIRCULATION SOCIETY
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